Idiopathic Pulmonary Fibrosis - Classification

Classification

Idiopathic pulmonary fibrosis is one specific presentation of idiopathic interstitial pneumonia (IIP), which is in turn a type of interstitial lung disease. Other forms of "idiopathic interstitial pneumonias" include non-specific interstitial pneumonia (NSIP), desquamative interstitial pneumonia (DIP) and acute interstitial pneumonia (AIP). Examples of known causes of interstitial lung disease include hypersensitivity pneumonitis, pulmonary Langerhans cell histiocytosis, asbestosis and collagen vascular diseases such as scleroderma and rheumatoid arthritis.

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