Transmissible Spongiform Encephalopathy - Classification

Classification

Known spongiform encephalopathies
ICTVdb Code Disease name Natural host Prion name PrP isoform
Non-human mammals
90.001.0.01.001. Scrapie Sheep and goats Scrapie prion OvPrPSc
90.001.0.01.002. Transmissible mink encephalopathy (TME) Mink TME prion MkPrPSc
90.001.0.01.003. Chronic wasting disease (CWD) Elk, White-tailed deer, Mule Deer and Red Deer CWD prion MDePrPSc
90.001.0.01.004. Bovine spongiform encephalopathy (BSE)
commonly known as "Mad Cow Disease"
Cattle BSE prion BovPrPSc
90.001.0.01.005. Feline spongiform encephalopathy (FSE) Cats FSE prion FePrPSc
90.001.0.01.006. Exotic ungulate encephalopathy (EUE) Nyala and greater kudu EUE prion NyaPrPSc
Human diseases
90.001.0.01.007. Kuru Humans Kuru prion HuPrPSc
90.001.0.01.008. Creutzfeldt-Jakob disease (CJD) CJD prion
(New) Variant Creutzfeldt-Jakob disease (vCJD, nvCJD) vCJD prion
90.001.0.01.009. Gerstmann-Sträussler-Scheinker syndrome (GSS) GSS prion
90.001.0.01.010. Fatal familial insomnia (FFI) FFI prion

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