Infantile Progressive Bulbar Palsy - Brown-Vialetto-Van-Laere Syndrome (pontobulbar Palsy With Deafness)

Brown-Vialetto-Van-Laere Syndrome (pontobulbar Palsy With Deafness)

Infantile progressive bulbar palsy
Classification and external resources
OMIM 211530

Brown-Vialetto-Van-Laere syndrome (BVVL) is a rare degenerative disorder that is characterized by progressive sensorineural deafness (Voudris 2002). BVVL is marked by a number of cranial nerve palsies including those of the motor components involving the 7th and 9th-12th cranial nerves, spinal motor nerves, and upper motor neurons (Voudris 2002).

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