Brown-Vialetto-Van-Laere Syndrome (pontobulbar Palsy With Deafness)
| Infantile progressive bulbar palsy | |
|---|---|
| Classification and external resources | |
| OMIM | 211530 |
Brown-Vialetto-Van-Laere syndrome (BVVL) is a rare degenerative disorder that is characterized by progressive sensorineural deafness (Voudris 2002). BVVL is marked by a number of cranial nerve palsies including those of the motor components involving the 7th and 9th-12th cranial nerves, spinal motor nerves, and upper motor neurons (Voudris 2002).
Read more about this topic: Infantile Progressive Bulbar Palsy
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