Endovascular Papillary Hemangioendothelioma

Endovascular Papillary Hemangioendothelioma

Endovascular papillary angioendothelioma (also known as a "Dabska tumor", "Dabska-type hemangioendothelioma," "Hobnail hemangioendothelioma," "Malignant endovascular papillary angioendothelioma," "Papillary intralymphatic angioendothelioma") is a rare low-grade angiosarcoma that presents as a slow-growing tumor on the head, neck, or extremity of infants or young children.

• Low power photomicrograph of an endovascular papillary angioendothelioma showing papillae with hyalinized cores

• High power view showing a vascular tumor with cuboidal endothelium lining the vessels. Few entrapped seminiferous tubules are also noted (arrow).