Congenital Hyperinsulinism - Terminology

Terminology

This condition has been referred to by a variety of names in the past 50 years. Nesidioblastosis and islet cell adenomatosis were favored in the 1970s, beta cell dysregulation syndrome or dysmaturation syndrome in the 1980s, and persistent hyperinsulinemic hypoglycemia of infancy (PHHI) in the 1990s.